KMID : 1130320080510010098
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Korean Journal of Pediatrics 2008 Volume.51 No. 1 p.98 ~ p.101
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Primary leiomyosarcoma of the chest wall in a child
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Choi Jae-Hyuk
Chung Chan-Wook Lee Mee-Jeong
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Abstract
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Leiomyosarcoma is an uncommon soft tissue sarcoma of mesenchymal cell origin, which shows smooth muscle differentiation. Leiomyosarcoma is seldom found in the pediatric population, and accounts for fewer than 2% of all soft tissue sarcomas. Leiomyosarcoma of the chest wall is extremely rare in children. We report here a case of an 8-year-old boy with a primary leiomyosarcoma that was incidentally found as a rib mass. The patient underwent a complete resection for a suspected osteochondroma diagnosed by a three-dimensional chest computed tomography examination. Pathological findings of the mass revealed intersecting fascicles of spindle cells showing cigar-shaped nuclei, inconspicuous nuclear pleomorphism and occasional mitotic figures in the background of a suspected osteochondroma of the rib. This report documents the first description of a leiomyosarcoma possibly arising in an osteochondroma
of the rib in a child. (Korean J Pediatr 2008;51:98-101)
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KEYWORD
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Leiomyosarcoma, Chest wall, Rib, Osteochondroma, Child
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